Quick Answer: What Foods Can A Person With Phenylketonuria Eat?

What foods do not contain protein?

The following are low-protein foods:all fruits, except dried fruits.all vegetables, except peas, beans, and corn.many sources of healthful fats, such as olive oil and avocados.herbs and spices..

What organs does phenylketonuria affect?

Without the enzyme, levels of phenylalanine build up in the body. This buildup can harm the central nervous system and cause brain damage.

How much phenylalanine is too much?

Doses higher than 5,000 milligrams a day can cause nerve damage. Risks. People with certain conditions should avoid using this supplement, including those with Schizophrenia (Tardive dyskinesia, a movement disorder, may develop.)

Can phenylketonuria be treated?

There is no cure for PKU, but treatment can prevent intellectual disabilities and other health problems. A person with PKU should receive treatment at a medical center that specializes in the disorder.

What is cystic fibrosis life expectancy?

However, fertility treatment is often a successful solution. The average life expectancy of a person with cystic fibrosis in the U.S. is approximately 37.5 years with many living much longer.

Do eggs contain phenylalanine?

Phenylalanine occurs naturally in many protein-rich foods, such as milk, eggs and meat. Phenylalanine is also sold as a dietary supplement.

Why is phenylalanine in food?

Phenylalanine is an amino acid found in many foods and used by your body to produce proteins and other important molecules. It has been studied for its effects on depression, pain and skin disorders.

How do you reduce phenylalanine?

The most effective treatment is restriction of phenylalanine in diet provided through different strategies including combination of low‐protein foods, hydrolyzing of protein‐rich foods, or use of protein substitutes.

What foods should be avoided with PKU?

People with PKU must avoid foods that are high in protein like meat, fish, poultry, dairy, soy, legumes (dried beans) or nuts. Some fruits and vegetables are higher in protein than others. PHE is in almost everything except sugar, salt, oil, and water.

What foods do not contain phenylalanine?

Foods such as meat, fish, eggs, milk, cheese, nuts and pulses are excluded as they contain high levels of phenylalanine. Vegetables and fruit are allowed in measured amounts only! Special low protein bread, pasta, biscuits and flour are used to supplement the diet and ensure adequate calorie intake.

What foods contain phenylalanine?

Phenylalanine is found in most protein-containing foods such as milk, eggs, cheese, nuts, soybeans, chicken, beef, pork, beans and fish.

What is the life expectancy of someone with PKU?

PKU does not shorten life expectancy, with or without treatment. Newborn screening for PKU is required in all 50 states.

Do you outgrow PKU?

A person with PKU does not outgrow it and must stay on the diet for life.

How does phenylketonuria affect the body?

Phenylketonuria (PKU) is a treatable disorder that affects the way the body processes protein. Children with PKU cannot use a part of the protein called phenylalanine. If left untreated, phenylalanine builds up in the bloodstream and causes brain damage.

What happens if someone with PKU eat protein?

A dangerous buildup of phenylalanine can develop when a person with PKU eats protein-rich foods, such as milk, cheese, nuts or meat, and even grains such as bread and pasta, or eats aspartame, an artificial sweetener. This buildup of phenylalanine results in damage to nerve cells in the brain.

Is phenylalanine the same as aspartame?

The ingredients of aspartame are aspartic acid and phenylalanine. Both are naturally occurring amino acids. Aspartic acid is produced by your body, and phenylalanine is an essential amino acid that you get from food. When your body processes aspartame, part of it is broken down into methanol.