How Common Are Infantile Spasms?

What is the best treatment for infantile spasms?

Treatment of infantile spasms has little class I data, but adrenocorticotropic hormone (ACTH), prednisolone and vigabatrin have the best evidence as first-line medications.

Other therapies including the ketogenic diet and other anti-epileptics medications may also prove useful in the treatment of infantile spasms..

Are infantile spasms an emergency?

These seizures should be considered a medical emergency due to the potentially devastating consequences on the developing brain, Dr. Mary Zupanc says.

What infantile spasms look like?

What are infantile spasms? Infantile spasms, sometimes called West syndrome, are a type of seizure that occurs in babies. The spasms look like a sudden stiffening of muscles, and the baby’s arms, legs, or head may bend forward. The seizures occur in a series of short spasms, about one to two seconds in length.

What does a infant seizure look like?

Focal seizures: Focal seizures may involve the infant having spasms or rigidity in one muscle group, becoming pale, sweating, vomiting, screaming, crying, gagging, smacking their lips, or becoming unconscious. For an example of how a focal seizure might look, click here.

Can babies grow out of infantile spasms?

They look very much like a startle. Babies also might have slowed development or loss of skills (like babbling, sitting, or crawling). Although the spasms usually go away by the time a child is 4 years old, many babies with IS will have other kinds of epilepsy later in life.

Are baby spasms normal?

Expect some of the following: Sudden jerks or twitches of the arms, hands or legs. If they only occur during sleep, they are most likely normal. How Long: last a few seconds, but can recur.

Is infantile spasms rare disease?

Symptoms. In 9 out of 10 children with the condition, infantile spasms happen in the first year of life, typically between 3 and 8 months of age. To begin with, the spasms are usually infrequent and do not happen in clusters. Therefore it is quite common for the diagnosis to be made quite late.

How often do infantile spasms occur?

Infantile spasms are not common. It affects around one out of three thousand infants. In about 20 percent of cases, the cause is not known. These infants most often develop normally.

How do I know if my baby has infantile spasms?

Symptoms of Infantile Spasms (IS)Raise their arms over their head or stick their arms straight out to the side.Stiffen their legs or “tuck them into the belly,” as if having stomach pain.Suddenly bend at the waist.Drop or bob their heads briefly.Roll their eyes back suddenly with subtle head nodding.More items…

Do babies cry when they have infantile spasms?

They might cry right before or right after they have a seizure. Your baby may also seem to twitch or jerk a muscle. You might hear the doctor call this myoclonus.

What are the signs to look for in neurological symptoms in infants?

Neonatal Neurological Disorder SymptomsFussiness.Decreased level of consciousness.Abnormal movements.Feeding difficulty.Changes in body temperature.Rapid changes in head size and tense soft spot.Changes in muscle tone (either high or low)

Can infantile spasm be cured?

Many children with infantile spasms develop other kinds of epilepsy. (Watch examples of infantile spasms.) “Some of these children can be cured, but successful treatment often depends on prompt diagnosis,” said Hussain.

At what age do infantile spasms start?

Infantile spasms, first described with a group of symptoms known as West syndrome, is a form of epilepsy ​that occurs in 1 in 2,000 children. It typically begins between 2-12 months of age and peaks between 4-8 months of age.

What happens if infantile spasms are left untreated?

Left untreated, infantile spasms can lead to serious outcomes, including an estimated infant mortality rate of between 5% and 6%. The most significant concern, however, is that infantile spasms are associated with autism and intellectual deficits that permanently affect quality of life.

Do infantile spasms occur daily?

In between clusters of spasms many hours without spasms can occur. Occasionally more than a day will pass without a cluster of spasms. Clusters of spasms often occur after waking from sleep, whatever time of the day. When an infant has a typical spasm, there are several movements.

Can infantile spasms go away on their own?

The sooner your little one starts treatment for infantile spasms or West syndrome, the better, because this condition can affect how their mind and body develop. In some cases, the seizures and spasms will stop on their own, but most children will need treatment.

Does West syndrome go away?

West syndrome (also called infantile spasms) should go away by the time your child is 4 years old. But most people who had it will get another kind of epilepsy or seizure condition in childhood or as an adult. About 1 in 5 will have Lennox-Gastaut syndrome, a severe form of epilepsy with multiple types of seizures.